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DeCS
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Descriptor English:
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Keratoderma, Palmoplantar, Diffuse
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Descriptor Spanish:
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Queratodermia Palmar y Plantar Difusa
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Descriptor Portuguese:
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Ceratodermia Palmar e Plantar Difusa
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Synonyms English:
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Keratosis Palmaris et Plantaris Familiaris
Syndrome, Thost-Unna
Syndrome, Unna-Thost
Thost Unna Syndrome
Thost-Unna Syndrome
Tylosis
Unna Thost Syndrome
Unna-Thost Syndrome
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Tree Number:
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C16.320.850.475.440
C17.800.428.435.440
C17.800.827.475.440
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Definition English:
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An autosomal dominant disorder characterized by a widely distributed, well-demarcated hyperkeratosis of the palms and soles. There is more than one genotypically distinct form, each of which is clinically similar but histologically distinguishable. Diffuse palmoplantar keratoderma is distinct from palmoplantar keratoderma (KERATODERMA, PALMOPLANTAR), as the former exhibits autosomal dominant inheritance and hyperhidrosis is frequently present. |
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Indexing Annotation English:
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do not confuse with KERATODERMA, PALMOPLANTAR
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History Note English:
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90
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Allowable Qualifiers English:
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Record Number:
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24759
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Unique Identifier:
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D015776
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Occurrence in VHL:
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Similar:
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DeCS
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